Berkhoff M Weis J Schroth G Sturzenegger M 2001 Extensive white matter signal changes were observed on T2-weighted images of a 49-year-old man. He presented with a slowly progressive gait disorder, and finally developed severe dementia. Extensive metabolic and infectious investigations failed to disclose the underlying cause during life. Autopsy revealed adult polyglucosan body disease. We discuss MRI findings likely to permit this diagnosis if combined with clinical findings and nerve or skin biopsy. https://sonar.ch/global/documents/6374 eng info:eu-repo/semantics/altIdentifier/doi/10.1007/s002340000425 info:eu-repo/semantics/altIdentifier/pmid/11305757 Neuroradiology. - 2001 Ataxia Biopsy Brain Diseases Dementia Diagnosis, Differential Disease Progression Glucans Humans Magnetic Resonance Imaging Male Middle Aged Skin Extensive white-matter changes in case of adult polyglucosan body disease. http://purl.org/coar/resource_type/c_6501