Journal article
Anesthesia management in a young child with aromatic l-amino acid decarboxylase deficiency.
- Vutskits L Department of Anesthesiology, Pharmacology and Surgical Intensive Care, University Hospital of Geneva, Geneva, Switzerland. Laszlo.Vutskits@hcuge.ch
- Menache C
- Manzano S
- Haenggeli CA
- Habre W
- 2006-01-18
Published in:
- Paediatric anaesthesia. - 2006
Anesthesia, General
Anesthetics, Inhalation
Aromatic-L-Amino-Acid Decarboxylases
Child, Preschool
Female
Humans
Infant
Methyl Ethers
Sevoflurane
English
Aromatic l-amino acid decarboxylase (AADC) deficiency is characterized by an almost complete absence of sympathetic autoregulation, because of very low levels of circulating catecholamines. Here, we report the successful management of four consecutive anesthesia procedures in a young child presenting with AADC deficiency. Our experience suggests that, with appropriate anticipation of the potential autonomic disturbances, anesthesia, at least for minor surgical and diagnostic procedures, can be conducted safely in patients with AADC deficiency.
- Language
-
- English
- Open access status
- closed
- Identifiers
-
- DOI 10.1111/j.1460-9592.2005.01605.x
- PMID 16409536
- Persistent URL
- https://sonar.ch/global/documents/205602
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